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We read with interest the description of Klippel-Trénaunay syndrome by Mameli et al1 in the July 2009 issue of Archives. While much of the description is informative, we would suggest that the cutaneous hallmark of the disease is the “capillary [lymphaticovenous] malformation” and is preferred over the term hemangioma.
Early literature on vascular birthmarks is complicated by indiscriminate application of terms such as hemangioma to denote heterogeneous vascular anomalies, including those now more specifically identified as capillary malformations (port-wine stains), cutis marmorata telangiectatica congenita, kaposiform hemangioendothelioma, and pyogenic granuloma, to name just a few.
Yan AC, Treat JR, Liang MG. Terminology Used to Describe Vascular Anomalies. Arch Pediatr Adolesc Med. 2010;164(2):203-205. doi:10.1001/archpediatrics.2009.274