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Article
October 1956

CONGENITAL ABSENCE OR ATRESIA OF A MAIN BRANCH OF THE PULMONARY ARTERY

Author Affiliations

Los Angeles
National Heart Institute Trainee, U.S. Public Health Service (Dr. Austin).; From the Children's Medical Group, Los Angeles, and the Departments of Pediatrics and Radiology, University of California School of Medicine at Los Angeles.

AMA Am J Dis Child. 1956;92(4):398-402. doi:10.1001/archpedi.1956.02060030392010
Abstract

THE CLINICAL diagnosis of congenital absence of a main branch of the pulmonary artery was first described by Madoff and associates1 in 1952. They found, however, that 9 cases had been recorded previously in which the diagnosis had been made at autopsy or operation. Since that time, only 23 additional patients have been reported,* bringing the total number of documented cases to 32. This figure does not include nine cases which have been mentioned in the literature but not reported.† We wish to report observations recently made in two patients with a functionally absent left pulmonary artery associated with tetralogy of Fallot.

Report of Cases  Case 1.—An 18-month-old Mexican boy entered the U.C.L.A. Medical Center on Jan. 12, 1956. He had apparently been well until 4 months of age when the parents first noted cyanosis while crying. During the remainder of the first year, cyanosis was visible only on

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