March 1960

Clitoral Enlargement Simulating Pseudohermaphroditism

Author Affiliations

From the Departments of Pediatrics and Gynecology, The Johns Hopkins University School of Medicine, and the Harriet Lane Home, The Johns Hopkins Hospital. Present address of Dr. Haddad is Section on Clinical Endocrinology, National Heart Institute, National Institutes of Health, Bethesda, Md.

AMA Am J Dis Child. 1960;99(3):282-287. doi:10.1001/archpedi.1960.02070030284005

Tumors of the clitoris are very rare, particularly in childhood.1 During the last three years, three children with tumors of the clitoris were referred to the pediatric endocrine clinic of the Harriet Lane Home at The Johns Hopkins Hospital with the diagnosis of pseudohermaphroditism. Each of the tumors, namely, a lipoma, a hemangioendothelioma, and a neurofibroma, is the first of its kind localized in the clitoris to be found in the literature. The purpose of this paper is to report these three cases with a brief comment on the diagnosis in relation to endocrine disorders and sexual anomalies.

Report of Cases  Case 1.—The patient, considered to be a male pseudohermaphrodite with a congenitally enlarged phallus, was one year old when referred for laparotomy. On physical examination, the clitoris was conspicuously enlarged (Fig. 1). It was clubshaped and measured 3.7 cm. in length and 2.1 cm. in diameter. The hypertrophy,

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