June 1966

Picture of the Month

Am J Dis Child. 1966;111(6):635-636. doi:10.1001/archpedi.1966.02090090107010

Denouement and Discussion 

HALLERMANN-STREIFF SYNDROME  (Dyscephalia Mandibulo-Oculo-Facialis, Dyscephalia of François)

MANIFESTATIONS  The head has an abnormal shape, usually brachycephalic or scaphocephalic. The frontal and parietal bones may be enlarged, and the fontanels remain open. The cranial vault appears enlarged in proportion to the small face. The nose is usually thin and beaked, with a sharp nasofrontal angle. There is striking micrognathia, and the mouth is small with thin lips and a high-arched palate. There are various dental abnormalities ranging from fully erupted teeth at birth to numerous malformed or absent teeth. Occasionally, there is limitation of opening of the mouth due to deformities of the temporomandibular joint. The ears are frequently low set; however, hearing

First Page Preview View Large
First page PDF preview
First page PDF preview