September 1966

Congenital Heart Disease and Pheochromocytoma

Author Affiliations

From the departments of pediatrics (Dr. Reynolds) and pathology (Dr. Gilchrist), Tulane University Medical School, and the Charity Hospital of Louisiana, New Orleans.

Am J Dis Child. 1966;112(3):251-255. doi:10.1001/archpedi.1966.02090120119014

IT IS RECOGNIZED that individuals with chronic cyanosis due to congenital heart disease are subject to a variety of medical complications. Among these are polycythemia, arterial thrombosis, anoxic seizures, brain abscess, hemorrhagic diathesis, dental caries, clubbing, bone changes,1 gout,2 and hydrarthrosis.3 Apparently pheochromocytoma is yet another complication.

Report of a Case  A 124/12-year-old white girl was first seen at Charity Hospital, New Orleans, at age 14 months. There was a history of 15 prior hospitalizations for cardiac failure and/or respiratory infections associated with cyanotic congenital heart disease.At 15 months cardiac catheterization was performed and a diagnosis of complete transposition of the great arteries and ventricular septal defect was made. Systemic arterial oxygen saturation was 30% to 50%. After discharge the patient was followed periodically in the cardiac clinic.At 5 years she developed severe jaundice, thymol turbidity was 37 units, and a diagnosis of infectious hepatitis

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