CONGENITAL pulmonary lymphangiectasis is the name applied by Laurence1 to a rare, usually fatal disease, characterized by dilated lymphatic channels in the subpleural and interlobular areas of the lungs of infants. Ekelund et al2 recently published a review of the literature and found 26 such cases. The present report deals with a full-term male infant who died in respiratory failure nine hours following birth and demonstrated congenital pulmonary lymphangiectasis at autopsy. This patient differs from those previously reported in that a pneumothorax was present.
Report of a Case
The patient was a full-term white male infant born by spontaneous vaginal delivery, without maternal anesthesia. It was the second uneventful pregnancy for the 20-year-old mother. The first stage of labor was four hours, the second stage of labor one half hour, and the membranes ruptured spontaneously one hour prior to delivery. The baby received an Apgar 10 on delivery
Brown MD, Reidbord HE. Congenital Pulmonary Lymphangiectasis. Am J Dis Child. 1967;114(6):654-657. doi:10.1001/archpedi.1967.02090270110014