THE cardiac anomaly in which the right pulmonary artery originates from the ascending aorta is a rare and usually fatal form of congenital heart disease. This lesion is often associated with a patent ductus arteriosus. Death frequently occurs in early infancy. However, it is a lesion that can be diagnosed during life and corrected with surgery. Twenty-five cases have been described in the literature.1-7 Nine of these patients have undergone surgical procedures with three survivors.1,3-5,7-11
The purpose of this paper is to present four additional cases of aortic origin of the right pulmonary artery including that of one infant who was successfully operated upon at 1 month of age.
Report of Cases
Case 1.—This 24-day-old male infant of Spanish-American extraction was born Jan 19, 1964 to a prima gravida 16-year-old mother after a normal pregnancy and uncomplicated delivery. The birth weight was 3.6 kg (7 lb 15 oz).
Stanton RE, Durnin RE, Fyler DC, Lindesmith GG, Meyer BW. Right Pulmonary Artery Originating From Ascending Aorta. Am J Dis Child. 1968;115(4):403-413. doi:10.1001/archpedi.1968.02100010405001