February 1973

Infantile Polycystic Disease of the Kidney

Author Affiliations

From the departments of radiology of Texas Children's Hospital, St. Luke's Episcopal Hospital, and the Texas Heart Institute, and Baylor University College of Medicine, Houston.

Am J Dis Child. 1973;125(2):167-170. doi:10.1001/archpedi.1973.04160020007002

Infantile sponge kidney is a rare form of congenital renal cystic disease characterized by hyperplasia of collecting tubules and a functioning nephron system. Roentgenographic appearance is pathognomonic and consists of bilaterally markedly enlarged kidneys with linear striations of contrast material on intravenous pyelograms.

Although the disease is fatal, most patients dying in infancy, survival may last for several years.