June 1974

The Mauriac Syndrome

Author Affiliations

From the departments of medicine (Dr. Mandell) and pediatrics (Dr. Berenberg), Children's Medical Center and Harvard Medical School, Boston.

Am J Dis Child. 1974;127(6):900-902. doi:10.1001/archpedi.1974.02110250126021

The Mauriac syndrome in florid form is an almost extinct disease. Its reappearance occurred in a 13-year-old diabetic girl. The classic features, including hepatomegaly, dwarfism, protuberant abdomen, moon-shaped face, and Cushingoid fat deposition, diminished after control with long-acting insulin and proper dietary management.