Normal numbers of B lymphocytes of all three major immunoglobulin classes were found in the peripheral blood of a 3-week-old boy with complete absence of serum IgA and IgM. The additional occurrence of acrodermatitis enteropathica suggests a possible relationship between this syndrome and the immune deficiency.
Pass RF, Johnston RB, Cooper MD. Agammaglobulinemia With B Lymphocytes in a Neonate With Acrodermatitis Enteropathica. Am J Dis Child. 1974;128(2):251–253. doi:10.1001/archpedi.1974.02110270125025