January 1975

Thoracic Coarctation Associated With Neurofibromatosis

Author Affiliations

From the departments of radiology (Drs. Rowen and Dorsey), pediatrics (Drs. Rowen and Kegel), and surgery (Dr. Ostermiller), Childrens Hospital of Orange County and St. Joseph Hospital, Orange, Calif; and University of California at Irvine.

Am J Dis Child. 1975;129(1):113-115. doi:10.1001/archpedi.1975.02120380083019

A child with neurofibromatosis and hypertension also demonstrated renal artery stenosis, the most common cause of hypertension in children with neurofibromatosis; abdominal coarctation, which has previously been described; and thoracic coarctation, which, to our knowledge, has not been previously reported. Rib notching may appear in patients with uncomplicated nueorfibromatosis, but the possibility of associated thoracic coarctation must also be considered in these patients.