A 12-year-old boy with classic dermatomyositis developed a rapidly progressive pulmonary process that led to his death a month later. Physiologically, there was interference with the oxygenation of the blood even when 100% oxygen was delivered to the lungs under pressure. Microscopic examination of the lungs disclosed diffuse interstitial pulmonary fibrosis. We conclude that these pulmonary changes were a component of the basic disease.
Park S, Nyhan WL. Fatal Pulmonary Involvement in Dermatomyositis. Am J Dis Child. 1975;129(6):723-726. doi:10.1001/archpedi.1975.02120430057016