June 1975

Fatal Pulmonary Involvement in Dermatomyositis

Author Affiliations

From the departments of pediatrics, Columbia-Presbyterian Medical Center, Babies Hospital, New York (Dr. Park); and University of California San Diego, School of Medicine, La Jolla (Dr. Nyhan).

Am J Dis Child. 1975;129(6):723-726. doi:10.1001/archpedi.1975.02120430057016

A 12-year-old boy with classic dermatomyositis developed a rapidly progressive pulmonary process that led to his death a month later. Physiologically, there was interference with the oxygenation of the blood even when 100% oxygen was delivered to the lungs under pressure. Microscopic examination of the lungs disclosed diffuse interstitial pulmonary fibrosis. We conclude that these pulmonary changes were a component of the basic disease.