January 1981

Inherited Disorders of Carbohydrate Metabolism

Author Affiliations

National Institute of Child Health and Human Development National Institutes of Health Clinical Center, 13N 260 Bethesda, MD 20014


edited by D. Burman, J. B. Holton, and C. A. Pennock, 433 pp, $39.50, Baltimore, University Park Press, 1980.

Am J Dis Child. 1981;135(1):87-88. doi:10.1001/archpedi.1981.02130250073034

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This monograph contains the proceedings of the 16th Annual Symposium on Inherited Disorders of Carbohydrate Metabolism of the Society for the Study of Inborn Errors of Metabolism, held in Bristol, England, July 12 to 14, 1978. About 25 invited speakers and 150 participants from Europe and North America contributed to this well-balanced conference, which so effectively combined clinical and scientific interests. The result is an excellent state-of-the-art presentation covering six interesting and important, albeit rare, disorders of carbohydrate metabolism. To be sure, this book fulfills the goals of the Society, which "exists to promote exchanges of ideas between workers in different disciplines who are interested in any aspect of inborn metabolic disorders."

Thus, in the first section, H. G. Hers presents a brilliant summary of the basic biochemistry of carbohydrate regulation as of 1978. This is followed in section 2 by two chapters on carbohydrate malabsorption, which tend to be

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