Access to paid content on this site is currently suspended due to excessive activity being detected from your IP address Please contact the publisher to request reinstatement.
November 1982

Choledochal Cyst Resulting in Congenital Cirrhosis

Author Affiliations

University of Tennessee Center for the Health Sciences and LeBonheur Children's Medical Center Memphis

Am J Dis Child. 1982;136(11):1025-1027. doi:10.1001/archpedi.1982.03970470069018

Choledochal cyst is a rare but remediable cause of neonatal cholestasis. This uncommon biliary malformation, although thought to be a congenital lesion, has seldom been diagnosed in the first month of life. We describe a 3-week-old infant with cholestasis caused by a choledochal cyst and associated with biliary cirrhosis.

Report of a Case.—A female infant was admitted to the hospital at 3 weeks of age for evaluation of conjugated hyperbilirubinemia. A 2,600-g newborn, she was noted to be jaundiced on the first day of life. The total serum bilirubin level was 10.5 mg/dL; at 7 days of age, it was 6.5 mg/dL. During the first three weeks of life, the infant gained 340 g, but she remained jaundiced and had pale stools.

She was a small, active, icteric infant with a firm liver that was palpable 3 cm below the right costal margin (span, 5 cm) and a

First Page Preview View Large
First page PDF preview
First page PDF preview