March 1985

Picture of the Month

Author Affiliations

Contributed from the National Birth Defects Center, 30 Warren St, Brighton, MA 02135.

Am J Dis Child. 1985;139(3):319-320. doi:10.1001/archpedi.1985.02140050113038

Denouement and Discussion 

Hemangioma and Lymphangioma of the Nose 

Manifestations  Major manifestation is a bulbous nose that has a "spongy-feel" on touch. A bluish color and/or the presence of superficial veins located on the skin of the affected area are secondary to the hemangioma. The hemangioma grows rapidly during the first year of life (usually the first six months) and then slowly resolves. However, because of the lymphangioma component, the nose does not return to normal size. Clinically it is difficult to determine if a lymphangioma component is present and is diagnosed by histologie examination. Frequently other hemangiomas and lymphangiomas are present, especially on the face.

Genetics  There is no evidence that the combination of lymphangioma and hemangioma of the nose is inherited in a mendelian fashion.

Treatment  Controversy exists regarding proper treatment, especially the hemangiomatous component. Treatment of the hemangioma may not be necessary because it frequently spontaneously resolves.

First Page Preview View Large
First page PDF preview
First page PDF preview