February 1990

Picture of the Month

Author Affiliations

Contributed from the Mary Black Memorial Hospital, Spartanberg, SC (Dr Elhassani), and Beilinson Medical Center, Tel-Aviv, Israel (Drs Lerman-Sagie, Mimouni, and Metzker).

Am J Dis Child. 1990;144(2):207-208. doi:10.1001/archpedi.1990.02150260087035

The statements listed below are best associated with which of the above figures:

  • (a) This condition is not associated with a tumor, and because it is difficult to treat, it may require amputation.

  • (b) An asymptomatic upper abdominal mass is present.

  • (c) Deep venous abnormalities are associated with this syndrome.

  • (d) In this condition, hemiatrophy, and not hemihypertrophy, is present.

Denouement and Discussion  (a) Proximal femoral focal deficiency (Fig 3) is a congenital defect of unknown cause, usually consisting of a shortening of the proximal portion of the femur, with or without involvement of the pelvic bones. The severity of the condition depends on the presence or absence of the femoral head and the acetabulum. Treatment is directed toward stabilizing the hip. Correction of the leg length discrepancy may require a Syme's amputation above the knee and then fitting with a prosthesis.(b) Wilms' tumor, one of the most common

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