September 1997

Picture of the Month

Author Affiliations

From the Departments of Dermatology, Yale University School of Medicine, New Haven, Conn (Dr Karlsson), Allegheny University of the Health Sciences, Philadelphia, Pa (Dr Telang); and the American Board of Pediatrics, Chapel Hill, NC (Dr Tunnessen).

Arch Pediatr Adolesc Med. 1997;151(9):949-950. doi:10.1001/archpedi.1997.02170460087016

At Birth, 3 infants had cutaneous lesions of varying severity. They were otherwise well. The infant in Figure 1 through Figure 3 had extensive lesions, while the other 2 infants (Figure 4 and Figure 5) had less extensive involvement of their skin.

Denouement and Discussion 

Cutis Marmorata Telangiectatica Congenita  Cutis marmorata telangiectatica congenita (CMTC) was first described by Van Lohuizen in 1922.1 The condition is an uncommon, localized or generalized, cutaneous vascular malformation that is usually present at birth. Though mostly sporadic, a few familial cases have been reported.2-4 Cutis marmorata telangiectatica congenita is a congenital abnormality that most often is manifested in the skin, but up to 50% of the patients of reported cases have an additional congenital or developmental abnormality, most often minor.2,5,6

CLINICAL FEATURES  The lesions of CMTC are usually present at birth or shortly thereafter, and appear as flat or depressed areas of

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