AN 8-YEAR-OLD GIRL was referred for evaluation of congenital facial deformities. She was born after an uneventful pregnancy during which her mother received no medications and was not exposed to radiation. There was no family history of congenital anomalies.
On physical examination the girl had unilateral macrostomia as a result of a transverse right stomal cleft and a severe deformity of the right auricle, including supernumerary auricular cartilage anterior to the tragus and absence of the right ear canal (Figure 1 and Figure 2). The left ear was normal. There was no evidence of midfacial skeletal hypoplasia. The ascending ramus of the mandible and the temporomandibular joint were normal. The palate was intact. Conductive hearing loss was present in the right ear. The remainder of the physical examination results were unremarkable.
Méndez R, Bello A, Aymerich H, Garrido M, Tunnessen WW. Picture of the Month. Arch Pediatr Adolesc Med. 1999;153(8):889-890. doi:10.1001/archpedi.153.8.889