SAMIR S.SHAHMDALBERT C.YANMD
A 10-week-old infant girl was referred to our hospital with a rapidly growing lesion involving the right orbit. The infant was twin B of nonidentical twins and born prematurely at 29 weeks' gestation. The lesion had been present at birth as a flat purplish mark and had started to increase in size from the age of 10 days. On examination, a large, soft periocular mass was observed and had been completely occluding the right eye from the age of 5 weeks (Figure 1 and Figure 2). The baby was otherwise well. A complete blood cell count and results of coagulation tests and a basic chemistry panel were all normal. Following further diagnostic investigations and therapeutic interventions, the infant required surgical treatment at the age of 17 weeks (Figure 3 and Figure 4).
Large periocular tumor causing complete occlusion of the right eye.
Presentation of the tumor in profile.
Excision of the major bulk of the tumor, measuring 4.5 × 3 × 2 cm.
Presentation at 10 weeks postsurgery.
What is your diagnosis?
Weibel L, Hoey S, Syed S, Harper JI, Dunaway D, Abou-Rayyah Y. Picture of the Month—Quiz Case. Arch Pediatr Adolesc Med. 2007;161(10):1001. doi:10.1001/archpedi.161.10.1001-a