Sign In
Individual Sign In
Create an Account
Institutional Sign In
OpenAthens Shibboleth
Citations 0
Special Feature
October 2007

Picture of the Month—Quiz Case

Author Affiliations



Copyright 2007 American Medical Association. All Rights Reserved. Applicable FARS/DFARS Restrictions Apply to Government Use.2007

Arch Pediatr Adolesc Med. 2007;161(10):1001. doi:10.1001/archpedi.161.10.1001-a

A 10-week-old infant girl was referred to our hospital with a rapidly growing lesion involving the right orbit. The infant was twin B of nonidentical twins and born prematurely at 29 weeks' gestation. The lesion had been present at birth as a flat purplish mark and had started to increase in size from the age of 10 days. On examination, a large, soft periocular mass was observed and had been completely occluding the right eye from the age of 5 weeks (Figure 1 and Figure 2). The baby was otherwise well. A complete blood cell count and results of coagulation tests and a basic chemistry panel were all normal. Following further diagnostic investigations and therapeutic interventions, the infant required surgical treatment at the age of 17 weeks (Figure 3 and Figure 4).

Figure 1.
Image not available

Large periocular tumor causing complete occlusion of the right eye.

Figure 2.
Image not available

Presentation of the tumor in profile.

Figure 3.
Image not available

Excision of the major bulk of the tumor, measuring 4.5 × 3 × 2 cm.

Figure 4.
Image not available

Presentation at 10 weeks postsurgery.

What is your diagnosis?