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Clinical Observation
January 2003

Presentation of Degos Syndrome as Acute Small-Bowel Perforation

Author Affiliations

From the Departments of Surgery (Drs Gonz[[aacute]]lez Valverde, Menarguez Pina, Mauri Barbera, Luri Prieto, Garc[[iacute]]a Marcilla, and V[[aacute]]zquez Rojas) and Pathology (Dr Ruiz) and the Intensive Care Unit (Dr G[[oacute]]mez Ramos), Hospital General Vega Baja, Servicio de Cirug[[iacute]]a General, Murcia, Spain.

Arch Surg. 2003;138(1):57-58. doi:10.1001/archsurg.138.1.57

Malignant atrophic papulosis is an uncommon vasculopathy affecting multiple systems and frequently associated with a poor prognosis. We describe a 56-year-old patient with this rare disorder whose death was the result of intestinal involvement. Clinical diagnostic features of malignant atrophic papulosis as well as the main therapeutic approaches suggested in the literature are presented herein.