Malignant atrophic papulosis is an uncommon vasculopathy affecting multiple systems and frequently associated with a poor prognosis. We describe a 56-year-old patient with this rare disorder whose death was the result of intestinal involvement. Clinical diagnostic features of malignant atrophic papulosis as well as the main therapeutic approaches suggested in the literature are presented herein.
González Valverde FM, Menarguez Pina F, Ruiz JA, Gómez Ramos MJ, Mauri Barbera F, Luri Prieto P, García Marcilla JA, Vázquez Rojas JL. Presentation of Degos Syndrome as Acute Small-Bowel Perforation. Arch Surg. 2003;138(1):57-58. doi:10.1001/archsurg.138.1.57