Few surgeons will ever encounter patients with EHE, a rare tumor. In this article, Cardinal and colleagues have summarized the current state of management for EHE and have shared their experience for treating patients with these unusual tumors. As they point out, there are no distinguishing characteristics for diagnosis, and these tumors can mimic a variety of other tumors. Careful pathologic analysis with appropriate tumor markers should be used to make the diagnosis, and appropriate imaging should be performed to evaluate for extrahepatic disease. Liver transplant is currently the most widely recommended therapy.
Hebert JC. Getting a Handlle on Managing Rare TumorsComment on “Treatment of Hepatic Epithelioid Hemangioendothelioma”. Arch Surg. 2009;144(11):1039. doi:10.1001/archsurg.2009.124