PRIMARY sarcoma of the esophagus is a rare condition. Dvorak1 in 1931 presented an excellent discussion of the entire subject and reviewed the reported cases up to that time. He found less than 50 cases in the literature, and in many of these there was considerable doubt concerning the exact pathologic process. Simon2 three years earlier was able to collect only about 30 unquestioned cases.
Since 1931 there have been few additional cases of primary sarcoma of the esophagus reported. Jaleski and Waldo3 described an interesting case of a primary melanotic sarcoma of the esophagus which was not diagnosed before autopsy. The tumor was polypoid, and there was extensive metastasis to the lungs, liver, pancreas, spine and regional lymph nodes. Cases of primary leiomyosarcoma of the esophagus have been contributed by Mallory,4 Menne and Birge,5 French and Garland6 and Pennes.7 Bayer8 in
CLARK DE. SARCOMA OF THE ESOPHAGUSReport of Successful Resection of a Fibrosarcoma. Arch Surg. 1949;59(2):348-354. doi:10.1001/archsurg.1949.01240040353016