There are many excellent reports in the literature dealing with the subject of congenital duodenal obstruction. This condition has been variously termed arteriomesenteric obstruction of the duodenum, chronic duodenal ileus, arteriomesenteric duodenal ileus, Wilkie's syndrome, and the superior mesenteric artery syndrome. Recent articles by Berley and Brown,1 Canlas,2 Kettenbach and Palumbo,3 Telford,4 and Findlay and Humphreys5 report a small series of cases with reviews of previous publications. Most authors seem to be agreed that this type of obstruction takes place because of one of three underlying defects: (1) congenital anomalies of the intestinal tract with variations from normal bowel rotation; (2) accentuation of the normal angulation at the duodenojejunal junction (ligament of Treitz), or (3) pressure and compression of the duodenum at the duodenojejunal junction by the superior mesenteric artery and vein, due to a foreshortened and tightened mesentery.
The following two cases are thought
ROTHENBERG RE. Congenital Duodenal ObstructionReport of Two Cases Occurring in Mother and Daughter, with Surgical Care. AMA Arch Surg. 1958;76(4):617-620. doi:10.1001/archsurg.1958.01280220137028