Persistent left superior vena cava has been merely a medical curiosity until recent years because it is uncommon and has little influence on hemodynamics. However, recent advances in cardiac surgery have brought the condition to prominence. It is important to recognize its existence before open heart surgery, for special arrangements have to be made for venous cannulation to get a completely dry field during total bypass.
Eight cases of congenital heart disease associated with persistent left superior vena cava were found in about 400 cases of congenital heart disease encountered in the Second Surgical Division of Okayama University Medical School. The superior vena cava was present on both sides in seven; in the case reported here, only a left superior vena cava was present with an absent normal inferior vena cava. Associated anomalies, atrial septal defect and pulmonicstenosis, were corrected under direct vision with the aid of extracorporeal circulation.
SUNADA T, INADA K, NAKANISHI M, KOMOTO Y. Left Superior Vena Cava With Anomalous Inferior Vena CavaReport of a Case With Associated Atrial Septal Defect and Pulmonic Stenosis, Successfully Corrected. Arch Surg. 1963;87(4):632-635. doi:10.1001/archsurg.1963.01310160094017