Although Hirschsprung's disease in the neonatal period is being recognized more frequently, complete aganglionosis of the colon is rare7 and presents a difficult diagnostic problem.10,16 Treatment of this condition can be successful if the diagnosis is established early.1,3,4,5,7,8
The following patient illustrates the problems encountered in such cases and describes a method of definitive treatment in the neonate.
Report of Case
A 13-day-old girl was admitted to the Hospital for Sick Children, Toronto, on April 18, 1963. Her chief signs were vomiting and abdominal distention, which had been noted a few days after birth.The baby had been born of a gravida IV mother who had had persistent nausea during her pregnancy. Labor and delivery were uneventful.Birth weight was 7 lb 10 oz (3,459 gm). She was started on breast feedings but did not nurse well. It was difficult to get the infant to take sufficient
DESJARDINS JG, SIMPSON JS. Neonatal Hirschsprung's DiseaseTreatment of Complete Aganglionosis of the Colon by the Duhamel Operation. Arch Surg. 1963;87(6):1019-1022. doi:10.1001/archsurg.1963.01310180135022