BECAUSE congenital atresia of the extrahepatic biliary tract is almost always fatal, exception to this course becomes of interest.
The remarkable history of one such infant was reported in 19601 when he had attained the age of 2½ years and, after three operations, he was in good health developing normally and free of jaundice. Since he is now 8½ years of age, has had two more operations, is still free of jaundice, and is again in good health, his further course since 1960 should be of interest.
He had an exploratory operation for jaundice at the age of 3 months; a diagnosis of congenital atresia of the extrahepatic biliary tract was made. At age 11 months he was found to have an intraperitoneal biliary cyst which was tapped at regular intervals for relief of what was considered to be ascites. This relieved his jaundice, decompressed his hepatic biliary tract,
SELIGMAN AM, ZUIDEMA GD. Congenital Atresia of the Extrahepatic Bile DuctsEight-Year Follow-Up After Successful Treatment. Arch Surg. 1966;92(6):822-824. doi:10.1001/archsurg.1966.01320240010003