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In this monograph the authors relate in detail four cases observed in the clinics of the Bohemian University in Prague and give a complete discussion of all phases of the disease. References are given to all reports published subsequent to Albert Schmidt's monograph of 1919. The heredity is direct and the tendency is recessive, but the disease tends to become more severe in successive generations. Males are about twice as frequently affected as females. The onset is usually at puberty, and in the thirties the attacks generally begin to decrease in frequency. The average duration of attacks is two days. The paralysis is symmetrical and most marked in the proximal parts of the limbs. The sphincters escape. Sensation is unaffected. In addition to the decrease or loss of electric responses during the attacks, certain myotonic and myasthenic features are demonstrable in the intervals. The authors consider the disease a muscular