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January 1932

PROGRESSIVE PALLIDAL DEGENERATION: A NEW CLINICOPATHOLOGIC SYNDROME

Author Affiliations

PHILADEPHIA

From the Graduate School of Medicine, University of Pennsylvania, the Laboratory of Neuropathology of the Philadelphia General Hospital and Temple University.

Arch NeurPsych. 1932;27(1):1-21. doi:10.1001/archneurpsyc.1932.02230130007001
Abstract

At the meeting of the Philadelphia Neurological Society in December, 1924, Dr. F. X. Dercum1 presented two brothers, each showing retinitis pigmentosa; the older had in addition a well marked extrapyramidal rigidity, and the younger had this condition in its incipiency. Dr. Dercum thought that the symptom group (the association of retinitis pigmentosa with rigidity) had not been described before. Since that presentation, the condition in both patients has progressed. The elder brother died in November, 1927, after an intense degree of rigidity had developed. The younger is still living. The brain and spinal cord of the elder brother were sent to my laboratory, where an intensive study was made. The history of the cases was supplied by Dr. Dercum.

CLINICAL REPORT OF CASES 

Case 1.  —W. D., the elder brother, was a white man, aged 24, at the time of death. His chief complaints were dimness of vision

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