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March 1941

ASTROCYTOSIS ARACHNOIDEAE CEREBELLI: A Rare Manifestation of von Recklinghausen's Neurofibromatosis

Author Affiliations


From the Division of Neurosurgery of the University of Chicago.

Arch NeurPsych. 1941;45(3):520-532. doi:10.1001/archneurpsyc.1941.02280150128010

Bizarre intracranial manifestations of von Recklinghausen's neurofibromatosis have been described frequently. The present case is a unique example of one of the peculiar lesions of this kaleidoscopic disease.

REPORT OF A CASE  R. N. L., a 16 year old girl, was admitted to the University of Chicago Clinics, to the service of Dr. A. Kenyon, on Aug. 6, 1939. She complained of severe headache during most of her life, aggravated recently and associated with nausea and vomiting, awkwardness and clumsiness for twelve years, urinary frequency and incontinence all her life and mental retardation.The patient was an only child of parents who separated when she was 4 years old. Both parents were in good health, and the family history was irrelevant except that the patient's maternal aunt and grandmother had multiple small tumors all over their bodies (neurofibromatosis?). In her early teens the patient's head became so large that her

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