According to Cushing and Bailey,1 Schuback was the first to refer to angiomatosis of the central nervous system as Lindau's disease. Lindau,2 in studying angiomatous nodules in cerebellar cysts, observed an association of this lesion with angiomatosis of the retina, otherwise known as von Hippel's disease, and by studying the reported cases of the latter disease he noted that it was not unusual to find a coincidental hemangioma of the cerebellum or of some other part of the nervous system (Lindau's disease). He considered it possible that the hemangioma of the cerebellum was only part of a systemic angioblastic disorder of the central nervous system often associated with a cystic pancreas, cystic kidneys and, more rarely, hypernephromas, tumors of the epididymis and angiomatosis of the liver. However, the abdominal lesions are not known to cause symptoms. The complete complex is rare.
Lindau's conception represents a newly recognized disorder,