THE WIDER recognition of the relationship between developmental anomalies of the skin and coexisting abnormalities of other ectodermal derivatives, particularly the nervous system, is important clinically. Early surgical relief when such lesions are compressing the adjacent structures of the central nervous system is imperative, and too long a delay causes irreparable damage. This has been repeatedly emphasized by a number of authors. As early as 1895 Berenbruch1 noted the relation of cutaneous angiomas, lipomas and vascular tumors of the spinal cord. He was able to demonstrate actual vascular connections between an angioma of the cervicothoracic portion of the spinal cord and multiple angiolipomas of the skin of the upper part of the trunk in a case reported at that time, the connecting vessels in that instance passing by way of the intervertebral foramens. Cushing and Bailey,2 in their monograph on vascular tumors, pointed out that the skin and