The term pseudo-pseudohypoparathyroidism is applied to a condition in which a patient with dyschondroplasia and ectopic bone formation responds to administration of parathyroid hormone. The patient here described, a 61-year-old woman, had a round facies, short stature, shortened metacarpals and metatarsals, symmetrical deformities of both elbows, and lens opacities. Her response to parathyroid hormone was not studied, but determinations of calcium and phosphorus in her blood suggested normal parathyroid function. Hospitalization was made necessary by excessive drowsiness associated with alveolar hypoventilation and obesity. The patient left the hospital much improved after achieving a weight-reduction of 9 kg. (20 lb.).
Casey TR, Fast BB, Cherniack RM. PSEUDO-PSEUDOHYPOPARATHYROIDISM: REPORT OF A CASE WITH ASSOCIATED CARDIOPULMONARY SYNDROME OF OBESITY. JAMA. 1959;169(17):1988–1990. doi:10.1001/jama.1959.03000340020005
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