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October 24, 1959


Author Affiliations

Madison, Wis.

Chief of Pathology and Director of Laboratories, Madison General Hospital, and Assistant Clinical Professor of Pathology, University of Wisconsin School of Medicine (Dr. Piper); Resident, Department of Pathology, Madison General Hospital (Dr. Frank).

JAMA. 1959;171(8):1094-1098. doi:10.1001/jama.1959.73010260001010

It is generally held that congenital cystic disease of the lung is of bronchial origin. However, since Virchow1 first described a similar lesion, thought to be of lymphatic origin, 21 such cases have been reported in the world literature. We wish to add two additional cases, one of which presents an unusual association of lymphatic cystic dilatation in other body organs.

As is often the case with new lesions, there are divergent points of view as to their etiology and the terminology to be applied to them. Laurence2 described congenital cystic disease of the lung as congenital pulmonary cystic lymphangiectasis, Giammalvo,3 as congenital lymphangiomatosis of the lung, and Maidman and Barnett,4 as congenital dilatation of pulmonary lymphatics.

It is apparent from a review of all cases that this entity, no matter by which name it is called, must be included with other disease processes responsible for