Reports of unusual cases are justified by the fact that each account further adds to the accumulated knowledge of a particular problem. With this in mind, a case of Kartagener's syndrome with lymphosarcoma of the small intestine is reported.
Kartagener's syndrome, sometimes referred to as K's triad, consists of situs inversus viscerum, bronchiectasis, and paranasal sinusitis. Reports in the literature of some cases of this syndrome, however, have represented the third member of the triad as agenesis of the frontal sinuses.1 In 1887 Fisher described total situs inversus, and in 1904 Siewert2 reported the first case of situs inversus with bronchiectasis in a 21-year-old male. In Vienna, Kartagener3 had, by 1935, collected 11 cases and added sinusitis to the organ transposition and pulmonary features, thus establishing the triad which bears his name today. Two years later, in 1937, Adams and Churchill4 published the first report of
Gude HE, Hull JE. KARTAGENER'S SYNDROME WITH LYMPHOSARCOMA OF SMALL INTESTINE. JAMA. 1959;171(13):1825–1828. doi:https://doi.org/10.1001/jama.1959.73010310001015
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