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November 15, 1976

Lymphangiomatosis With Splenic Involvement

Author Affiliations

From the departments of pediatrics (Drs Avigad, Jaffe, and Rotem), radiology (Dr Izhak), and pathology (Dr Frand), the Chaim Sheba Medical Center, Tel-Hashomer, and the Sackler School of Medicine, University of Tel Aviv, Tel Aviv, Israel.

JAMA. 1976;236(20):2315-2317. doi:10.1001/jama.1976.03270210041022

Severe splenomegaly and anemia developed in a 5-year-old girl with diffuse lymphangiomatosis of the upper part of the body. Radioisotope scanning and celiac angiography demonstrated lymphangiomatosis of the spleen, a rare but diagnosable condition. Intractable infection in areas of ulcerated skin led to her death from overwhelming sepsis.

(JAMA 236:2315-2317, 1976)