Shulman's syndrome includes fasciitis of rapid onset, sclerodermoid skin changes, absence of Raynaud's phenomenon, absence of visceral manifestations of progressive systemic sclerosis, hypergammaglobulinemia, transient eosinophilia, and a dramatic response to systemic corticosteroid therapy. Although this syndrome may be a variant of scleroderma, its dramatic responsiveness to corticosteroid therapy is a particularly distinguishing feature.
(JAMA 240:451-453, 1978)
Fu TS, Soltani K, Sorensen LB, Levinson D, Lorincz AL. Eosinophilic Fasciitis. JAMA. 1978;240(5):451–453. doi:10.1001/jama.1978.03290050041015
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