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Article
September 30, 1911

MYOTONIA ATROPHICA: WITH A REPORT OF TWO CASES

Author Affiliations

Chief of Clinic, Neurological Institute; Clinical Assistant, Neurological Institute NEW YORK

JAMA. 1911;LVII(14):1117-1118. doi:10.1001/jama.1911.04260090339008
Abstract

The symptom-complex to which Rossolimo1 gave the name of "myotonia atrophica" is not only an extremely rare disease, but apparently is exceptionally uncommon in America, the two cases reported in 1908 by Ramsay Hunt2 being the only ones on record. Batten and Gibb,3 in 1909, collected reports of all the cases which had been described under various titles up to that time, which showed the rather definite clinical picture of myotonia atrophica. They were able to enumerate twenty, and as a result of their study state the following as the cardinal symptoms of the disease:

1. Weakness and wasting of the following muscles, viz.: the orbicular muscles of the mouth and eyes; the temporals and masseters; the vasti muscles of the thighs with the recti femuris frequently escaping completely; the muscles of the anterior tibial groups, resulting in bilateral foot-drop.

2. The myotonic phenomenon evidenced more particularly

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