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Article
August 3, 1901

THE MORBID ANATOMY OF PROGRESSIVE MUSCULAR DYSTROPHY.

JAMA. 1901;XXXVII(5):330. doi:10.1001/jama.1901.02470310036002
Abstract

The pathology of the group of diseases comprehended in the designation progressive muscular dystrophy and including so-called idiopathic, hereditary, juvenile or scapulo-humeral, infantile or facio-scapulo-humerai muscular atrophy and pseudohypertrophic muscular paralysis is yet surrounded in dense obscurity. For a time confusion with progressive muscular atrophy of spinal origin existed clinically, but postmortem examinations failed to disclose the characteristic lesion of this disease. Such anatomic abnormalities as have been found were not uniform or distinctive and the most probable explanation is that the disease represents some defect in development. A case somewhat confirmatory of this view has recently been reported by Dr. Jenö Kollarits.1 The patient was a boy, 10 years old, presenting the pseudohypertrophic type of progressive muscular dystrophy, the exact time of the beginning of which could not be determined. He had been totally helpless and unable to walk for more than two years, and contractures were marked.

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