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JAMA Cardiology Clinical Guidelines Synopsis
August 2018

Management of Ventricular Arrhythmias and Sudden Cardiac Death Risk Associated With Cardiac Channelopathies

Author Affiliations
  • 1Division of Cardiology and Duke Clinical Research Institute, Duke University Hospital, Durham, North Carolina
  • 2Cardiovascular Division, Vanderbilt University Medical Center, Nashville, Tennessee
JAMA Cardiol. 2018;3(8):775-776. doi:10.1001/jamacardio.2018.1116

Although cardiac channelopathies account for only 3% of sudden cardiac deaths (SCDs) that occur in young people, they have been the focus of much research because of their traumatic effect on families and society.1 Many advances have been made in the diagnosis, risk stratification, and treatment of these conditions that have informed practices and formed the foundation of professional guidelines and statements.2,3 One such guideline is the American Heart Association (AHA)/American College of Cardiology (ACC)/Heart Rhythm Society (HRS) Guideline for Management of Patients With Ventricular Arrhythmias and the Prevention of Sudden Cardiac Death, the focus of this synopsis.3 This guideline covered the following cardiac channelopathies: long QT syndrome (LQTS), catecholaminergic polymorphic ventricular tachycardia (CPVT), Brugada syndrome, early repolarization, and short QT syndrome.3

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