Progressive hemifacial atrophy (HFA) is a rare craniofacial disorder characterized by progressive atrophy of the skin, subcutis, muscles, and bone. Classified on a spectrum with frontoparietal linear morphea/en coup de sabre (ECDS), HFA occurs deep, with atrophy of the subcutis, muscle, and bone. Features of ECDS and HFA often coexist,1 and the 2 entities are considered variants of craniofacial localized scleroderma.2