TEMPI (telangiectasias, erythrocytosis with elevated erythropoietin, monoclonal gammopathy, perinephric fluid collections, intrapulmonary shunting) syndrome is a recently described rare plasma cell neoplasm with paraneoplastic features.1,2 In this case report, we describe a patient with TEMPI syndrome with classic and atypical cutaneous findings that track with the progression of pulmonary symptoms.
Lor M, Cheng M, Liang B, Cheng CE. TEMPI Syndrome With Progressive Telangiectasias Associated With Pulmonary Deterioration. JAMA Dermatol. 2020;156(12):1379–1380. doi:10.1001/jamadermatol.2020.2668
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