TEMPI (telangiectasias, erythrocytosis with elevated erythropoietin, monoclonal gammopathy, perinephric fluid collections, intrapulmonary shunting) syndrome is a recently described rare plasma cell neoplasm with paraneoplastic features.1,2 In this case report, we describe a patient with TEMPI syndrome with classic and atypical cutaneous findings that track with the progression of pulmonary symptoms.
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Lor M, Cheng M, Liang B, Cheng CE. TEMPI Syndrome With Progressive Telangiectasias Associated With Pulmonary Deterioration. JAMA Dermatol. 2020;156(12):1379–1380. doi:10.1001/jamadermatol.2020.2668
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