Naevus syringadenomatosus papilliferus (Werther1), or naevus syringocystadenomatosus papilliferus, appears to be a rare dermatosis when judged by the few cases reported in the United States. Weidman2 described a section showing the typical structure; the nevus was discussed by McCarthy.3 The only case report from this country which we have found was published by Stokes,4 who discussed the clinical and histologic features of the dermatosis and gave several references to prior investigations. Reports of cases from foreign countries are somewhat more numerous: the pathogenesis was well described by Gans,5 Kyrle,6 Dörffel7 and Cardenal.8 Recently, cases have been reported by Fessler,9 Biberstein,10 Dörffel,7 and González Medina and Bigne.11
Frieboes12 gave a résumé of the clinical features of the disease. According to him, the favorite sites are the shoulders, the axillae, the genito-inguinal and surrounding regions and the
SACHS W, LEWIS GM. NAEVUS SYRINGADENOMATOSUS PAPILLIFERUS (WERTHER)REPORT OF FIVE CASES. Arch Derm Syphilol. 1937;36(6):1202–1209. doi:10.1001/archderm.1937.01480060075014
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