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Article
July 1938

INCONTINENTIA PIGMENTI (BLOCH-SULZBERGER): REPORT OF AN ADDITIONAL CASE, WITH COMMENT ON POSSIBLE RELATION TO A NEW SYNDROME OF FAMILIAL AND CONGENITAL ANOMALIES

Author Affiliations

NEW YORK, New York, Richmond Hill, N. Y.

From the Skin and Cancer Unit, New York Post-Graduate Medical School and Hospital, Columbia University, service of Dr. J. Frank Fraser.

Arch Derm Syphilol. 1938;38(1):57-69. doi:10.1001/archderm.1938.01480130060009
Abstract

In 1928 one of the present authors1 reported and discussed the first case of the rare and peculiar dermatosis incontinentia pigmenti. His detailed report originated in the department of dermatology of the University of Zurich, Switzerland, and the patient had previously been presented by Bloch,2 of Zurich, at the meeting of the Swiss Dermatologic Society in 1925.

Subsequently, at the tenth meeting of the Swiss Dermatologic Society, Naegeli,3 of Berne, Switzerland, reported three analogous cases. In Naegeli's brief report familial occurrence, as well as the combination of the pigmentary anomaly with another familial dermatosis, was demonstrated for the first time. A father and two daughters, 12 and 9 years of age, presented the pigmentary dermatosis, while a third child suffered from a cutaneous disease which Naegeli diagnosed as hydroa vacciniforme.

A fifth case of incontinentia pigmenti was reported by Almquist.4 In Almquist's case a boy of

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