There is an extensive and controversial literature on the "disease of the mammary areola preceding cancer of the mammary gland" to which Paget called attention. Even more disagreement is evident concerning what has been reported as extramammary Paget's disease. Some authors have ruled out the possibility of Paget's disease occurring outside the nipple as contrary to definition, while others have cited cases of extramammary involvement as strong evidence for their conception of the disease. It appears necessary to review briefly the various definitions and conceptions of Paget's disease before reporting 3 cases on which we shall base our discussion of the subject.
Paget's disease was first conceived as a clinical entity, and little has been added to Paget's original outline of the clinical signs and symptoms. Paget1 described the disorder as an eroded and weeping, a crusty eczematoid or a dry psoriasiform eruption of the mamilla and areola. The
PINKUS H, GOULD SE. EXTRAMAMMARY PAGET'S DISEASE AND INTRAEPIDERMAL CARCINOMA. Arch Derm Syphilol. 1939;39(3):479–502. doi:10.1001/archderm.1939.01480210094010
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