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January 1947

EPIDERMOLYSIS BULLOSA: A Recently Described Variant

Arch Derm Syphilol. 1947;55(1):91-100. doi:10.1001/archderm.1947.01520010095010

SINCE Pels and Goodman1 described their case of a bullous type of Darier's disease, many similar reports have appeared, but under different titles. "Familial benign chronic pemphigus" was recorded by Hailey and Hailey2; Ayres and Anderson3 called the disease "recurrent herpetiform dermatitis repens"; the term "dyskeratoid dermatosis" was used by Frank and Rein,4 and Franks and Traub5 suggested the term "familial benign chronic bullous dermatosis." Many cases are recorded in recent American literature.6

The aforementioned cases are similar as regards histories, clinical pictures and microscopic data, and most observers agree that they are instances of the same disease. The profusion of names indicates that the exact nature of the disease is not agreed on. This is largely due to different interpretations of the histologic observations. We do not propose to contribute a new legend, but we shall attempt to show that the disease is