Because of its extreme rarity it was deemed worth while to report this case of dermatomyositis associated with hypertrichosis. Dermatomyositis is a rare disease characterized by a nonsuppurative inflammation and degeneration of the striated musculature and associated with diverse cutaneous changes and vasomotor signs similar to Raynaud's phenomenon. It is frequently unrecognized because of its variable clinical manifestations. The disease may have an acute or insidious onset, with frequent remissions and exacerbations, but is eventually fatal in about half the cases. There is no sex predominance, and the age range is usually between 10 and 50 years.1
Cutaneous changes2 are prevalent and include erythema, edema, pigmentation, sclerosis, atrophy, lupus erythematosus-like efflorescence and poikiloderma atrophicans vasculare. Keil3 minutely described the cutaneous and mucomembranous lesions. However, the microscopic changes are not considered specific for this disorder.1
Muscular involvement may produce pain, tenderness, stiffness and fatigue. Serious outcome may be
REICH NE, REINHART JB. DERMATOMYOSITIS ASSOCIATED WITH HYPERTRICHOSIS. Arch Derm Syphilol. 1948;57(4):725–732. doi:10.1001/archderm.1948.01520170123012
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