INCONTINENTIA pigmenti is a rare congenital anomaly. It was first fully described under this name by Sulzberger1 in 1927, and by Siemens2 in 1929 as ``melanosis corii degenerativa.'' Sulzberger's case had been previously presented by Bloch3 in 1925, and Siemens' case was discussed first in a dissertation by Lechleuthner.4 According to Becker,5 the condition was evidently described first by Bardach6 as a systematized nevus. Carney7 recently reviewed 32 cases from the literature (including the one reported in this paper) and added 5 more of his own. Additional cases are reported by heilesen8 (two cases), Jaramillo and his associates,9 Doornink10 (three cases), and Uebel and his co-workers11; the last authors cited two additional observations (Hora, Gerard). This would bring the total to about 46 cases of incontinentia pigmenti. Actually the number of cases presented is greater, because
EPSTEIN S, VEDDER JS, PINKUS H. BULLOUS VARIETY OF INCONTINENTIA PIGMENTI (BLOCH-SULZBERGER). AMA Arch Derm Syphilol. 1952;65(5):557–567. doi:10.1001/archderm.1952.01530240049007
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