BULLOUS VARIETY OF INCONTINENTIA PIGMENTI (BLOCH-SULZBERGER)

INCONTINENTIA pigmenti is a rare congenital anomaly. It was first fully described under this name by Sulzberger¹ in 1927, and by Siemens² in 1929 as ``melanosis corii degenerativa.'' Sulzberger's case had been previously presented by Bloch³ in 1925, and Siemens' case was discussed first in a dissertation by Lechleuthner.⁴ According to Becker,⁵ the condition was evidently described first by Bardach⁶ as a systematized nevus. Carney⁷ recently reviewed 32 cases from the literature (including the one reported in this paper) and added 5 more of his own. Additional cases are reported by heilesen⁸ (two cases), Jaramillo and his associates,⁹ Doornink¹⁰ (three cases), and Uebel and his co-workers¹¹; the last authors cited two additional observations (Hora, Gerard). This would bring the total to about 46 cases of incontinentia pigmenti. Actually the number of cases presented is greater, because