The following case report is presented because of the comparative rarity of this nevus. To our knowledge, only eight reports of this condition have appeared in the world's literature, only two in America.
Nevus lipomatodes cutaneus superficialis was the title given by Hoffmann and Zurhelle1 to a nevoid anomaly consisting of grouped papules and nodules which on histologic examination showed the presence of ectopic fatty tissue in the corium. The second case was described by Robinson and Ellis in 1937.2 In more recent years cases have been presented by Nikolowski,3 Kúta,4 Thöne,5 Holtz,6,7 Blumenthal,8 and Hering.9
Enough similarity exists in the clinical and histologic findings in all reported cases that there can be little doubt that this is an entity. Usually, at least part of the nevus had been present at birth, though there has often been extension of
LYNCH FW, GOLTZ RW. Nevus Lipomatosus Cutaneus Superficialis (Hoffmann-Zurhelle): Presentation of a Case and Review of the Literature. AMA Arch Derm. 1958;78(4):479–482. doi:10.1001/archderm.1958.01560100055008
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