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March 1959

Multiple Progressive Vascular Hamartomata of the Leg Simulating Kaposi's Hemorrhagic Sarcoma: Report of a Case

Author Affiliations


From the Department of Dermatology, College of Medicine, University of Cincinnati.

AMA Arch Derm. 1959;79(3):336-339. doi:10.1001/archderm.1959.01560150078012

The term hamartoma refers to benign tumors of embryonal origin. It designates tumor-like malformations showing a faulty mixture of the normal components of the organ in which they occur. The pattern and arrangement of these normal cells do not conform to the structural organization of the organ affected. The tumor is usually encapsulated. It is the disorganization, overgrowth, and encapsulation of these masses which makes them anomalous.1 Hamartomata may occur in any organ of the body but are commonest in the spleen, liver, kidney, lung, and pancreas. In the skin they may be recognized as vascular hamartomata.

Several syndromes have been described in which vascular hamartomata of the skin are associated with visceral lesions. In Maffucci's syndrome vascular hamartomata are associated with phlebectasia, enchrondromata, dyschrondroplasia, and "spider hands." Sturge-Weber syndrome2 consists of nevus flammeus in the distribution of one or more branches of the trigeminal nerve, glaucoma,

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