Incontinentia Pigmenti. Presented by Dr. Orlando Canizares.
A boy aged 5½ years has lesions which were first noticed at birth. There has been no appreciable change recently.
There is a peculiarly distributed pigmentation on the sides of the face, extremities, and trunk. The lesions tend to appear in a bizarre configuration along the extremities, forming lines or angles with sharp outlines. There is a faint, papular, lichenoid eruption, more pronounced on the cheeks. A vague, irregular alopecia is present.
Dr. Wilbert Sachs: For want of any other diagnosis I will agree. However, I have never seen this linear pigmentation in incontinentia pigmenti. I have seen several cases of that disorder, but it occurred in patches and not in streaks up and down the legs.
Dr. M. J. Costello: That was my impression at first, but the eruption is generalized and systematized, with a segmental distribution,
NEW YORK DERMATOLOGICAL SOCIETY. AMA Arch Derm. 1959;79(6):740–744. doi:10.1001/archderm.1959.01560180114034
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